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· 분류 : 외국도서 > 의학 > 소아과학
· ISBN : 9783540442059
· 쪽수 : 296쪽
· 출판일 : 2003-12-03
목차
1 Normal Bone Marrow.- References.- 2 Inherited Bone Marrow Failure.- Inherited Hematopoietic Syndromes Associated with Pancytopenia.- Fanconi Anemia.- Laboratory Findings.- Dyskeratosis Congenita.- Laboratory Findings.- Shwachman-Diamond Syndrome.- Laboratory Findings.- Congenital Amegakaryocytic Thrombocytopenia.- Laboratory Findings.- Rare Familial Marrow Failure Syndromes.- Inherited Hematopoietic Syndromes Associated with Single Cytopenia.- Diamond-Blackfan Anemia.- Laboratory Findings.- Congenital Dyserythropoietic Anemias.- Severe Congenital Neutropenia.- Laboratory Findings.- Cyclic Neutropenia.- Laboratory Findings.- Chronic Benign Neutropenia.- Thrombocytopenia with Absent Radii.- Laboratory Findings.- Inherited Disorders of the Leukocytes Associated with Change in their Morphology.- Pelger-Huet Anomaly.- May-Hegglin Anomaly.- Chediak-Higashi Syndrome.- Alder-Reilly Anomaly.- Other Morphological Abnormalities.- Inherited Immunodeficiency.- Reticular Dysgenesis (Alymphocytic Neutropenia).- Laboratory Findings.- X-Linked Agammaglobulinemia (Bruton Agammaglobulinemia).- Laboratory Findings.- Cartilage-Hair Hypoplasia.- Laboratory Findings.- Wiskott-Aldrich Syndrome.- Laboratory Findings.- Omenn Syndrome.- Laboratory Findings.- Inherited Sideroblastic Anemias.- Laboratory Findings.- ?-Aminolevulinate Synthase (ALAS2) Deficiency.- Pearson Syndrome.- Osteopetrosis.- Laboratory Findings.- References.- 3 Macrophage- and Dendritic-Cell-Related Disorders Including the Lysosomal Storage Disorders.- Storage Disorders.- Gaucher Disease.- Laboratory Findings.- Niemann-Pick Disease.- Laboratory Findings.- Wolman Disease.- Fabry Disease.- Sialidoses.- Gangliosidosis GM1 and GM2.- Fucosidosis.- OC-Mannosidosis.- Glycogen Storage Diseases.- Mucopolysaccharidosis.- Cystinosis.- Primary Hyperoxaluria.- Sea-blue Histiocytosis.- Histiocytosis.- Langerhans Cell Histiocytosis.- Laboratory Findings.- Xanthoma Disseminatum.- Macrophage-Related Disorders.- Hemophagocytic Syndrome.- Laboratory Findings.- References.- 4 Bone Marrow Infections.- Infection-Associated Hemophagocytic Syndrome.- Granulomas.- Bacterial Infections.- Mycobacteria.- Ehrlichiosis.- Fungus.- Viruses.- Human Parvovirus B19.- Epstein-Barr-Virus.- Cytomegalovirus.- Human Immune Deficiency Virus.- Human Herpesvirus Type 6.- Other Viruses.- Parasites.- Malaria.- Other Parasites.- References.- 5 Bone Marrow Metastases.- Laboratory Findings.- Neuroblastoma.- Laboratory Findings.- Rhabdomyosarcoma.- Laboratory Findings.- wing Family of Tumors.- Laboratory Findings.- Desmoplastic Small Round-Cell Tumor.- Central Nervous System.- Laboratory Findings.- Other Metastatic Tumors.- References.- 6 Hematologie Manifestations of Trisomy 21.- Laboratory Findings.- Acute Megakaryoblastic Leukemia (FAB M7).- Laboratory Findings.- Cytochemistry and Immunocytochemistry.- Electron Microscopy.- Cytogenetic and Molecular Genetics.- References.- 7 Myelodysplastic Syndromes.- Myelodysplastic and Myeloproliferative Disorders.- Myelodysplastic Syndromes.- Juvenile Myelomonocytic Leukemia.- Laboratory Findings.- Monosomy 7 Syndrome.- Unclassifiable Myelodysplastic Syndromes.- MDSs that Fit the FAB Classification in Children.- Laboratory Findings.- Myeloproliferative Disorders.- Chronic Myelogenous Leukemia.- Laboratory Findings.- Chronic Neutrophilic Leukemia.- Polycythemia Disorders.- Polycythemia Vera.- Laboratory Findings.- Essential Thrombocythemia.- Laboratory Findings.- Hypereosinophilic Syndrome/ Chronic Eosinophilic Leukemia.- Laboratory Findings.- Systemic Mastocytosis.- Laboratory Findings.- References.- 8 Acute Myeloid Leukemia.- Acute Myelogenous Leukemia.- Laboratory Findings.- Acute Myeloid Leukemia.- with Minimal Differentiation (FAB Mo).- Acute Myeloid Leukemia without Maturation (FAB M1).- Acute Myeloid Leukemia with Maturation (FABM2).- Acute Promyelocytic Leukemia (FAB M3).- Acute Myelomonocytic Leukemia (FAB M4).- Acute Monoblastic Leukemia (M5).- Acute Erythroleukemia (M6).- Acute Megakaryoblastic Leukemia (M7).- Acute Basophilic Leukemia.- Minimal Residual Disease.- Therapy-Related Acute Leukemia.- Congenital Leukemia.- Recurrent Chromosomal Abnormalities.- Acute Leukemia of Ambiguous Lineage.- References.- 9 Acute Lymphoblastic Leukemia and Lymphoma.- Acute Lymphocytic Leukemia/ Lymphoblastic Lymphoma.- Laboratory Findings.- Minimal Residual Disease.- Lymphomas.- Non-Hodgkin Lymphomas.- Large-Cell Lymphomas.- Anaplastic Large-Cell Lymphoma.- Laboratory Findings.- Hodgkin Lymphoma.- Laboratory Findings.- References.- 10 Anemias.- Microcytic Anemias.- Iron Deficiency Anemia.- Laboratory Findings.- Macrocytic Anemias.- B12 and Folk Deficiency.- Laboratory Findings.- Normocytic Anemias.- Hemolytic Anemias.- Hereditary Hemolytic Anemias.- Red Blood Cell Membrane Disorders.- Hereditary Spherocytosis.- Laboratory Findings.- Hereditary Elliptocytosis Syndromes.- Laboratory Findings.- Other Inherited Disorders of the Red-Cell Membrane.- Hereditary Anemias Due to Hemoglobin Abnormalities.- Sickle Cell Anemia.- Laboratory Findings.- Thalassemia Syndromes.- ?-Thalassemias.- Laboratory Findings.- ?-Thalassemias.- Acquired Hemolytic Anemia.- Hemolytic Disease of Newborn.- Laboratory Findings.- Autoimmune Hemolytic Anemia.- Laboratory Findings.- Acquired Non-Immune Hemolytic Anemias.- Paroxysmal Nocturnal Hemoglobinuria.- Transient Erythroblastopenia of Childhood.- Aplastic Anemia.- Laboratory Findings.- References.














